
Danilo Bilches Medinas
Staff Scientist
Instituto de Neurociencia Biomedica
Santiago, Chile
Free Radicals and Oxidants; Protein Misfolding and Aggregation; Cellular Stress; Cell Signaling; Neurodegenerative Diseases; Neurodevelopmental Disorders; Gene Therapy.
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Biochemistry, UNIVERSIDADE DE SAO PAULO. Brasil, 2010
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Chemistry, UNIVERSIDADE DE SAO PAULO. Brasil, 2005
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Postdoctoral Fellow Full Time
STANFORD UNIVERSITY
Palo Alto, Estados Unidos
2010 - 2011
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postdoc Full Time
UNIVERSIDAD DE CHILE
Santiago, Chile
2012 - 2015
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Staff Scientist Full Time
Instituto de Neurociencia Biomedica
Santiago, Chile
2015 - At present
1. Giselle Aimé Espinosa Vásquez, Evaluation of the impact of conditional genetic ablation of Pdia3 on the cognitive capacity of mice. Director. Undergraduate Thesis in Biochemistry. University of Santiago de Chile. Ongoing.
2. José Vicente González Teuber, Study of the contribution of IRE1? signaling to experimental amyotrophic lateral sclerosis (ALS). Co-director. PhD Thesis in Biomedical Sciences. University of Chile. Ongoing.
3. Pablo Sebastián Rozas Rojas, Effects of Erp57 Overexpression in a Mutant Sod1 Mouse Model of Amyotrophic Lateral Sclerosis. Co-director. Master Thesis in Biological Sciences. University of Chile. 2017.
4. Martín Nicolás Sepúlveda Durand, Characterization of Transgenic Mouse Lines for Mutant Forms of ERp57 Associated to Amyotrophic Lateral Sclerosis. Co-director. Undergraduate Thesis of Molecular Biotechnology Engineering. University of Chile. 2015.
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Travel Award
Society for Free Radical Biology and Medicine
Uruguay, 2007
Travel Award from the Society for Free Radical Biology and Medicine to present the work entitled “An Alternative Mechanism for Carbonate Radical Generation during Cu,ZnSod Peroxidase Activity”.
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Travel Award
Society for Free Radical Biology and Medicine
Estados Unidos, 2009
Travel Award from the Society for Free Radical Biology and Medicine to present the work entitled “MS Characterization of the Human Sod1 Covalent Dimer Produced from the Enzyme Peroxidase Activity. Implication to ALS”.
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Dean’s Fellowship
STANFORD UNIVERSITY
Chile, 2010
Postdoctoral Fellowship
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FAPESP Fellowship
FAPESP
Brasil, 2005
Doctorate Fellowship
Desafíos en el diagnóstico de enfermedad de Creutzfeldt-Jakob: Caso clínico |
ER stress links aging to sporadic ALS |
ERp57 as a novel cellular factor controlling prion protein biosynthesis: Therapeutic potential of protein disulfide isomerases |
DEFINING THE CONTRIBUTION OF ERP57 MUTANTS TO THE PATHOGENESIS OF AMYOTROPHIC LATERAL SCLEROSIS |
DEFINING MECHANISMS AND THE ROLE OF AGGREGATION OF WILD-TYPE SUPEROXIDE DISMUTASE 1 (SOD1) IN AMYOTROPHIC LATERAL SCLEROSIS |
Therapeutic Use of delta Protein Kinase C in Parkinson's Disease |
Aldehyde Dehydrogenase Activators as Novel Drugs For the Treatment of Parkinson's Disease |
Papéis de Oxidantes e Radicais Livres em Esclerose Lateral Amiotrófica (ELA). Implicações em Outros Processos Neurodegenerativos. |
Proteostasis disturbance in amyotrophic lateral sclerosis |
The ER proteostasis network in ALS: Determining the differential motoneuron vulnerability |

Claudio Hetz
Deputy Director
INSTITUTO DE CIENCIAS BIOMÉDICAS, FACULTAD DE MEDICINA, UNIVERSIDAD DE CHILE
SANTIAGO, Chile

Ute Wohlbier
Associate Professor
Center for Integrative Biology
Universidad Mayor de Chile
Santiago, Chile

Catherine Andreu
Estudiante de Doctorado
Escuela de Psicología
Pontificia Universidad Católica de Chile
Santiago, Chile

JUAN PABLO HENRIQUEZ
Associate Professor
Cell Biology
UNIVERSIDAD DE CONCEPCIÓN, FACULTAD DE CIENCIAS BIOLÓGICAS, DEPARTAMENTO DE BIOLOGÍA CELULAR
Concepción, Chile

Felipe Court
Full Professor and Director
Center for Integrative Biology
Universidad Mayor
Huechuraba, Chile

sandra espinoza
asistente de investigacion
Laboratorio Neuroinmunologia
Fundacion Ciencias para la Vida/Universidad San Sebastian
Santiago, Chile

Jose Matamala
Assistant Professor of Neurology
Department of Neurological Science
University of Chile
Santiago, Chile

Ariel Castro
Full Professor
Department of Biochemistry and Molecular Biology
UNIVERSIDAD DE CONCEPCION
concepciòn, Chile

Karina Palma
Postdoctorado
Instituto de Neurociencia Biomédica BNI
Universidad de Chile
Santiago, Chile

Melissa Calegaro
Principal Investigator, head lab
Research Vice Presidency
Universidad Mayor
Santiago, Chile

Jorge Ojeda
Académico investigador
Ciencias Básicas y Morfología
Universidad Católica de la Santisima Concepción
Concepción, Chile

Agustin Martinez
Profesor Titular
Instituto de Neurociencia
UNIVERSIDAD DE VALPARAÍSO, CENTRO INTERDISCIPLINARIO DE NEUROCIENCIAS DE VALPARAÍSO
Valparaíso, Chile

Víctor Cornejo
Profesor Asistente
Facultad de Ciencias Biológicas
Pontificia Universidad Católica de Chile
Santiago, Chile

Cristina Pinto
Doctor en ciencias biologicas
Centro de Biotecnología
Universidad de Concepción
Concepción, Chile

Valentina Castillo
Investigadora Postdoctoral
Instituto de Ingeniería Biológica y Médica
Pontificia Universidad Católica de Chile
Santiago, Chile

Brigitte van Zundert
Full Professor
UNIVERSIDAD ANDRÉS BELLO, CENTRO DE INVESTIGACIONES BIOMÉDICAS
Santiago, Chile

Pablo Henny
Profesor Asociado
Anatomía Normal
Pontificia Universidad Católica de Chile
Santiago, Chile

Ricardo Armisen
Associate Professor
Centro de Genética y Genómica
Universidad del Desarrollo
Santiago, Chile

Claudia Duran-Aniotz
Profesor Asociado
Escuela de Psicología
Universidad Adolfo Ibánez
Santiago, Chile
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Alicia Colombo
Profesora Asociada/Director Científico Biobanco de Tejidos y Fluidos de la Universidad de Chile
Departamento de Anatomía Patológica
Universidad de Chile
Santiago, Chile

Francisco Fuentes
Profesor Asistente
Departamento de Microbiología
Universidad de Concepción
Concepción, Chile

Nelson Osses
Associated Professor
Institute of Chemistry
PONTIFICIA UNIVERSIDAD CATÓLICA DE VALPARAÍSO
Valparaíso, Chile

Fabiola Osorio
Associate Professor
Programa Disciplinario de Inmunologia
Universidad de Chile
Santiago, Chile